Why a New Diagnostic Criteria for Pediatric Familial Mediterranean Fever Patients?
نویسندگان
چکیده
Familial Mediterranean fever (FMF) is a systemic auto-inflammatory disorder characterized by seemingly unprovoked recurrent episodes of fever and localized inflammation usually involving the peritoneum, pleura and joints accompanied by a marked acute-phase response. The disease primarily affects populations living around the Mediterranean basin ( Jewish, Armenian, Arab, Turkish populations) but is also scattered throughout the western world due to extensive population movements of the 20th century [1,2]. Although FMF is an ancient disease and the most common inherited Abstract
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Familial Mediterranean Fever: Review of Literature and Report of Two Cases
Familial Mediterranean fever, an autosomal recessive disorder, is a member of the periodic fever syndromes, and considered to be the most common cause of recurrent febrile episodes in children. It is important to understand the disorder as familial Mediterranean fever falls on a spectrum of various presentations; the recurrent episodes of familial Mediterranean fever may be so severe that the q...
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